Selected articles on ARVD/C in the medical literature published from January 2000 through January 2009. Many abstracts are available by searching PUBMED

FURTHER READING ON ARVD/C

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GENETICS

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PATHOLOGY

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Johns Hopkins Hospital
The Arrhythmogenic Right Ventricular Dysplasia Program
Publications

Manuscripts

  1. Tandri H, Rutberg J, Bluemke D, Calkins H.  Magnetic resonance imaging of arrhythmogenic right ventricular dysplasia.  J Cardiovasc Electrophysiol  2002; 13(11):1180.
  2. Nasir K, Bomma C, Khan F, Tandri H, Tichnell C, James C, Berger R, Calkins H. Utility of a Combined Signal-Averaged Electrocardiogram and QT Dispersion  
    Algorithm in Identifying Arrhythmogenic Right Ventricle Dysplasia in Patients with
    Tachycardia of Right Ventricle Origin.  Am J Cardiol 2003; 92(1):105-9.
  3. Nasir K, Tandri H, Rutberg J, Tichnell C, Spevak P, Crossan J, Baughman KL, Kasper EK, Tomaselli GF, Berger R, Calkins H.  Filtered QRS duration on SAECG predicts inducibility of ventricular tachycardia in Arrhythmogenic right ventricle dysplasia.  PACE 2003;(10):1955-1960.
  4. Nasir K, Rutberg J, Tandri H, Berger R, Tomaselli G, Calkins H.  Utility of SAECG in Arrhythmogenic right ventricular dysplasia. Ann Noninvasive Electrophysiol 2003 Apr;8(2):112-120.
  5. Marcus F, Towbin JA, Zareba W, Moss A, Calkins H, Brown M, Gear K; ARVD/C Investigators.  Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C):  a multidisciplinary study:  design and protocol.  Circulation 2003 Jun 17;107(23):2975-8.
  6. Tandri HS, Calkins H, Nasir K, Castillo E, Lima J, Rutberg J, Tichnell C, Bluemke D.  Magnetic resonance imaging findings in patients meeting task force criteria for Arrhythmogenic right ventricular dysplasia.  J Cardiovasc Electrophysiol 2003;(5):483-4.
  7. Tandri H, Calkins H, Marcus FI. Controversial role of magnetic resonance imaging in the diagnosis of arrhythmogenic right ventricular dysplasia.  Am J Cardiol 2003 Sept;92:(5)649. 
  8. Roguin A, Bomma C, Nasir K, Tandri H, Tichnell C, James C, Rutberg J, Crosson J, Spevak J, Berger R, Halperin H, Calkins H.  Implantable Cardioverter-Defibrillators in Patients with Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy.  J Am Coll Cardiol  2004;43(10):1843-52. 
  9. Bomma C, Rutberg J, Tandri H, Nasir K, Tichnell C, James C, Lima J, Bluemke D, Calkins H.  Misdiagnosis of Arrhythmogenic Right Ventricular Dysplasia (ARVD).  J Cardiovasc Electrophysiol2004;15(3):300-306.
  10. Tandri H, Friedrich M, Calkins H, Bluemke D.  MRI of Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia.  J Cardiovasc Magn Reson Imaging 2004; 6(2):557-563.
  11. Tandri H, Bomma C, Calkins H, Bluemke D.  Magnetic Resonance and Computed Tomography Imaging of Arrhythmogenic Right Ventricular Dysplasia.  J Magn Reson Imaging, 2004;19(6):848-58.
  12. Castillo E, Tandri H, Rodriguez ER, Nasir K, Calkins HG, Bluemke DA..  Arrhythmogenic right ventricular Dysplasia:  Ex Vivo and In Vivo Fat Detection with Black-Blood MR Imaging.  Radiology 2004;232(1):38-48.
  13. Nasir K, Calkins H.  Arrhythmogenic Right Ventricle Dysplasia/Cardiomyopathy.  ACC Current Journal Review 2004;06.002;28-33.
  14. Roguin A, Zviman M, Meininger G, Rodriques R, Dickfeld T, Bluemke D, Lardo A, Berger R, Calkins H, Halperin H.  Modern Pacemaker and Implantable Cardioverter-Defibrillator Systems can be MRI safe:  In-vitro and In-vivo assessment of safety and function at 1.5-Tesla.  Circulation 2004;110(5):475-482.
  15. Nasir K, Bomma C, Tandri H, Roguin A, Dalal D, Prakasa K, Tichnell C, James C, Spevak PJ, Marcus F, Calkins H.  Electrocardiographic Features of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy According to Disease Severity:  A need to broaden diagnostic criteria.  Circulation 2004 Sep21;110(12):1527-34.
  16. Tandri H, Ferrari VA, Bomma C, Khurram N, Blumeke D, Lima J, Calkins H. Findings on Magnetic Resonance Imaging of Idiopathic Right Ventricular Outflow Tachycardia:  Is There Evidence for Structural Heart Disease?  Am J Cardiol 2004;94(11):1441-5.
  17. Tandri H, Saranathan M, Rodriquez R, Martinez C, Bomma C, Nasir K, Rosen B, Lima J, Calkins H, Blumeke D.   Non-Invasive Detection of Myocardial Fibrosis in Arrhythmogenic Right Ventricular Cardiomyopathy Using Delayed-Enhancement MR Imaging.  J Am Coll Cardiol 2005 Jan 4;45(1):98-103.
  18. Yoerger D, Marcus F, Sherrill D, Calkins H, Towbin J, Zareba W, Picard M.  Echocardiographic Findings in Patients Meeting Task Force Criteria for Arrhythmogenic Right Ventricular Dysplasia.  J Am Coll Cardiol 2005 March 15;45(6):860-5.
  19. Bomma C, Dalal D, Tandri H, Prakasa K, Nasir K, Roguin A, Tichnell C, James C, Lima JAC, Calkins H, Bluemke DA. Regional Differences in Systolic & Diastolic Function in Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy (ARVD/C) using Magnetic Resonance Imaging.  Am J Cardiol 2005 June 15;95(12):1507-11.
  20. Piccini JP, Nasir K, Bomma C, Tandri H, Dalal D, Tichnell C, James C, Crosson J, Calkins H.  Electrocardiographic Findings Over Time in Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy.  Am J Cardiol 2005 July 1;96(1):122-6.
  21. Fritz J, Soliayappan M, Tandri H, Bomma C, Gence A, Joao JAC, Bluemke DA.  Right Ventricle Shape and Contraction Patterns and Relationship to MRI Findings. J Comput Assist Tomogr 2005 November/December;29(6):725-733.
  22. Piccini JP, Dalal D, Roguin A, Bomma C, Cheng A, Prakasa K, Dong J, Tichnell C, James C, Russell S, Crosson J, Berger R, Marine J, Tomaselli G, Calkins H.  Predictors of Appropriate Implantable Defibrillator Therapies in Patients with Arrhythmogenic Right Ventricular Dysplasia.  Heart Rhythm 2005 Aug 2;(11)1188-94.
  23. Dalal D, Nasir K, Bomma C, Prakasa K, Tandri H, Piccini J, Roguin A, Tichnell C, James C, Russell SD, Judge DP, Abraham T, Spevak PJ, Bluemke DA, Calkins H. Arrhythmogenic right ventricular dysplasia: a United States experience. Circulation. 2005 Dec 20;112(25):3823-32.
  24. Prakasa K, Calkins H.  Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy Review.  Curr Treat Options Cardiovasc Med., 2005 Dec;7(6):467-75
  25. Prakasa K, Dalal D, Bomma C, Wang J, Tandri H, James C, Tichnell C, Dong J, Russell S, Spevak P, Corretti M, Bluemke D, Calkins H, Abraham T.  Feasibility and Variability of Three Dimensional Echocardiography in Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy. Am J Cardiol March 2006 1;97(5)703-9
  26. Dalal D, Molin L, Piccini J, Tichnell C, James C, Bomma C, Prakasa K, Towbin J, Marcus F, Spevak P, Bluemke D, Abraham T, Russell S, Calkins H, Judge D.  Clinical Features of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy Associated with Mutations in Plakophilin-2.   Circulation 2006 Apr 4;113(13):1641-9.
  27. Bilchick K, Judge D, Calkins H, Marine J.  Use of a Coronary Sinus Lead and Biventricular ICD to Correct a Sensing Abnormality in a patient with Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy.  J Cardiovasc Electrophysiol March 2006 Vol. 17;317-320.
  28. Fritz J, Tandri H, Rodriquez R, Calkins H, Bluemke D.  Evaluation and course of an unusual case of arrhythmogenic right ventricular dysplasia.  Case Report, The Intl J Cardiovasc Imag  June 2006 Vol. 22:269-273.
  29. Awad MM, Dalal D, Cho E, Alarcon NA, James C, Tichnell C, Tucker A, Russell SD, Bluemke DA, Dietz HC, Calkins H, Judge DP.  DSG2 mutations contribute to Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy.  Am J Hum Genet. 2006 Jul;79(1):136-42.  Epub 2006 Apr 28.
  30. Tandri H, Castillo E, Ferrari V, Nasir K, Rutberg J, Lima J, Calkins C, Bluemke D.  MR imaging of Arrhythmogenic right ventricular dysplasia:  Observer agreement for qualitative and quantitative interpretation.  J Am Coll Cardiol. 2006 Dec 5;48(11):2277-84.
  31. Tandri H, Daya SK, Nasir K, Bomma C, Lima JA, Calkins H, Bluemke DA.  Normal Reference Values for the Adult Right Ventricle by Magnetic Resonance Imaging.  Am J Cardiol. 2006 Dec 15;98(12):1660-4.  Epub 2006 Oct 27
  32. Awad MM, Dalal D, Tichnell C, James C, Tucker A, Abraham T, Spevak PJ, Calkins H, Judge DP.  Recessive Arrhythmogenic Right Ventricular Dysplasia due to Novel Cryptic Splice Mutation in PKP2.  Hum Mutat. 2006 Nov;27(11):1157.
  33. Dalal D, James C, Devanagondi R, Tichnell C, Tucker A, Prakasa K, Spevak P, Bluemke D, Abraham T, Russell S, Calkins H, Judge D.  Penetrance of Mutations in Plakophilin-2 among Families with Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy.  J Am Coll Cardiol. 2006 Oct 3:48(7):1416-24.  Epub 2006 Sep 12.
  34. Calkins H.  Arrhythmogenic right ventricular dysplasia/cardiomyopathy. Curr Opin Cardiol. 2006 Jan; 21(1):55-63.
  35. Tandri H, Bomma C, Calkins H.  Unusual Presentation of Cardiac Sarcoidosis.  Congest Heart Fail. 2007 Mar-Apr;13(2):116-8.
  36. Macedo R, Prakasa K, Tichnell C, Marcus F, Calkins H, Lima JA, Bluemke DA.  Marked lipomatous infiltration of the right ventricle:  MRI findings in relation to arrhythmogenic right ventricular dysplasia. AJR Am J of Radiology. 2007 May;188(5):W423-7.
  37. Bomma C, Dalal D, Tandri H, Prakasa K, Nasir K, Roguin A, Piccini J, Dong J, Mahadevappa M, Tichnell C, James C, Lima JA, Fishman E, Calkins H, Bluemke DA.  Evolving role of multidetector computed tomography in evaluation of arrhythmogenic right ventricular dysplasia/cardiomypathy.  Am J Cardiol. 2007 Jul ;100(1):99-105.
  38. Dalal D, Jain R, Tandri H, Dong J, Eid SM, Prakasa K, Tichnell C, James C, Abraham T, Russell SD, Sinha S, Judge DP, Bluemke DA, Marine JE, Calkins H. Long-term efficacy of catheter ablation of ventricular tachycardia in patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy. J Am Coll Cardiol. 2007 Jul 31;50(5):432-40.
  39. Prakasa KR, Wang J, Tandri H, Dalal D, Bomma C, Chojnowski R, James C, Tichnell C, Russell S, Judge D, Corretti M, Bluemke D, Calkins H, Abraham TP. Utility of tissue Doppler and strain echocardiography in arrhythmogenic right ventricular dysplasia/cardiomyopathy.  Am J Cardiol. 2007 Aug 1;100(3):507-12.
  40. Wang J, Prakasa K, Bomma C, Tandri H, Dalal D, James C, Tichnell C, Corretti M, Bluemke D, Calkins H, Abraham TP.  Comparison of novel echocardiographic parameters of right ventricular function with ejection fraction by cardiac magnetic resonance.  J Am Soc Echocardiogr. 2007 Sep;20(9):1058-64.
  41. Tandri H, Macedo R, Calkins H, Marcus F, Cannom D, Scheinman M, Daubert J, Estes M 3rd, Wilber D, Talajic M, Duff H, Krahn A, Sweeney M, Garan H, Bluemke DA; Multidisciplinary Study of Right Ventricular Dysplasia Investigators. Role of magnetic resonance imaging in arrhythmogenic right ventricular dysplasia: insights from the North American arrhythmogenic right ventricular dysplasia (ARVD/C) study. Am Heart J. 2008 Jan;155(1):147-53.
  42. Awad MM, Calkins H, Judge DP. Mechanisms of Disease: Molecular Genetics of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy. Nature Clin Pract Cardiovasc Med. 2008 Apr 1:1-10.
  43. Judge DP and Johnson NM. Genetic Evaluation of Familial Cardiomyopathy.  Journal of Cardiovascular Translational Research, 2008; DOI 10.1007/s12265-008-902501.
  44. Tandri H, Asimaki A, Dalal D, Saffitz JE, Halushka MK, Calkins H. Gap Junction Remodeling in a Case of Arrhythmogenic Right Ventricular Dysplasia Due to a Plakophilin-2 Mutation. J. Cardiovasc Electrophysiol. 2008 Jun 12.
  45. Jain A, Tandri H, Calkins H, Bluemke DA. Role of cardiovascular magnetic resonance imaging in arrhythmogenic right ventricular dysplasia.  J Cardiovasc Magn Reson. 2008 Jun 20;10(1):32.
  46. Muthappan P, Calkins H. Arrhythmogenic right ventricular dysplasia. Prog Cardiovasc Dis. 2008 Jul-Aug;51(1):31-43.
  47. Calkins H. Progress continues in our understanding of the electrocardiographic manifestations of arrhythmogenic right ventricular dysplasia. J Cardiovasc Electrophysiol. 2008 Aug;19(8):782-3.
  48. Calkins H. Arrhythmogenic right ventricular dysplasia. Trans Am Clin Climatol Assoc. 2008;119:273-86; discussion 287-8.
  49. Calkins H, Marcus F. Arrhythmogenic right ventricular cardiomyopathy/dysplasia: an update. Curr Cardiol Rep. 2008 Sep;10(5):367-75.

Book Chapters

  1. Calkins H, Marcus F.  Arrhythmogenic right ventricular dysplasia/cardiomyopathy. In: Braunwald E, ed., Harrison’s Advances in Cardiology.  New York, NY: McGraw Hill, 2003:378-383.
  2. Tandri H, Bluemke DA. Assessment of Right Ventricular Dysplasia, In: Current Protocols in Cardiovascular Magnetic Resonance Imaging.  John Wiley & Sons, Inc., 2003: A10.2.1-A10.2.17.
  3. Calkins and Marcus. Ventricular Arrhythmias in ARVD/C  In:Gussak, I, Antzelovitch C, Wilde AAM ed in Electrical Diseases of the Heart; Genetics, mechanisms, treatment and prevention.  Springer London 2007.
  4. Jain R, Calkins H. Right ventricular dysplasia. In: Ventricular arrhythmias and sudden cardiac death. Blackwell, Chapter 5, 2008.

Abstracts

  1. Castillo E, Rutberg J, Wu KC, Bluemke DA.  Arrhythmogenic right ventricular dysplasia/cardiomyopathy: variability in protocols and image quality between MRI centers.  Circulation  2001;104 (Suppl II):640.
  2. Castillo E, Rutberg J, Wu KC, Bluemke DA.  Arrhythomogenic right ventricular dysplasia/cardiomyopathy: differences in protocols and image quality between MRI centers.  Radiology  2001; 221(P):360.
  3. Castillo E, Rutberg J, Braga HJV, Calkins H, Bluemke DA.  Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy:  Protocol Optimization of Black and Bright-Blood Techniques.  Proceedings of the 9th Scientific Meeting and Exhibition of the ISMRM, Berkeley, CA:  ISMRM 2001;1813.
  4. Nasir K, Rutberg J, Tandri H, Calkins H.  Filtered QRS duration on SAECG predicts inducibility of ventricular tachycardia in Arrhythmogenic right ventricle dysplasia.  PACE  2003;26(10):1955-60.
  5. Rutberg J, Nasir K, Tandri H, Bluemke D, Castillo E, Calkins H.  Mis-Diagnosis of Right Ventricular Dysplasia Due to Cardiac MRI Interpretations and Incomplete Evaluations.  PACE 2002;25(4)II:197.
  6. Tandri H, Fetics B, Nasir K, Rutberg J, Calkins H, Kass DA.  Fourier shape analysis of the right ventricle in Arrhythmogenic right ventricular dysplasia. PACE  2002;25(4)II:196.
  7. Tandri H, Griffith L, Tang T, Nasir K, Vasamreddy C, Berger R, Halperin H, Leng C, Tomaselli G, Calkins H, Donahue K.  Predictors of Mortality and Appropriate Therapy in a 20-Year Experience with Implantable Defibrillators.  PACE 2002;25(4)II:483.
  8. Nasir K, Rutberg J, Tandri H, Calkins H.  Value of a combined SAECG and QT dispersion algorithm in arrhythmogenic right ventricular tachycardia. Circulation  2002;106(19):2278
  9. Tandri H, Nasir K, Rutberg J, Lima J, Bluemke D, Spevak P, Calkins H.  Absence of regional abnormalities in idiopathic ventricular tachycardia by quantitative MRI analysis. Circulation 2002;106(19)3225.
  10. Bomma C, Tandri H, Nasir K, Tichnell C, James C, Lima J, Calkins H, Bluemke D.  Regional differences in diastolic function in arrhythmogenic right ventricular Dysplasia.  PACE 2003;26(4)II:734;1112.
  11. Bomma C, Tandri H, Nasir K, James C, Tichnell C, Fishman E, Calkins H, Bluemke D.  Role of helical CT in qualitative & quantitative evaluation of arrhythmogenic right ventricular dysplasia. PACE 2003;26(4)II:147;965.
  12. Nasir K, Bomma C, Roguin A, Tandri H, Tichnell C, James C, Berger R, Tomaselli G, Calkins H.  Filtered QRS duration predicts implanted cardioverter defibrillator (ICD) firing in patients with arrhythmogenic right ventricular dysplasia.  PACE 2003;26(4)II:60;943.
  13. Roguin A, Zviman M, Meininger G, Dickfeld T, Berger R, Calkins H, Halperin H.  Effect of Magnetic Resonance Imaging on Pacemaker and AICD Systems.  PACE 2003;26(4)II:122;959.
  14. Tandri H, Griffith L, Tang T, Nasir K, Capps M, Calkins H, Donahue K.  Clinical Course and Long-term Follow-up of Patients Receiving Implantable Cardioverter-Defibrillators.  PACE 2003;26(4)II:252;991.
  15. Tandri HS, Bomma C, Calkins H, Nasir K, Tichnell C, James C, Lima J, Bluemke D.  MR imaging findings in patients meeting task force criteria for Arrhythmogenic right ventricular dysplasia.  PACE  2003;26(4)II:145;965. 
  16. Nasir K, Rutberg J, Tandri H, Tichnell C, Berger R, Calkins H.  Prolonged S wave duration in V1-V3 is the most accurate EKG diagnostic marker for arrhythmogenic right ventricle dysplasia. J Am Coll Cardiol  2003; 41:100A.
  17. Tandri H, Griffith L, Tang T, Nasir N, Vasamreddy C, Tomaselli G, Halperin H, Leng C, Berger R, Calkins H, Donhue K.  Antiarrhythmic agents may decrease long term survival in patients with implantable defibrillators.  J Am Coll Cardiol  2003;41:1064-6.
  18. Bomma C, Roguin A, Tandri H, Tichnell C, James C, Rutberg J, Spevak P, Crosson J, Berger R, Halperin H, Calkins H.  Cardioverter-Defibrillators in Patients with Arrhythmogenic Right Ventricular Dysplasia.  Circulation  2003; 108:1793.
  19. Nasir K, Tufail K, Bomma C, Tandri H, Roguin A, Tichnell C, James C, Kasper E, Halperin H, Spevak P, Calkins H.  ECG and SAECG Predictors of Disease Severity, VT Induction and Implantable Defibrillator Firing in Arrhythmogenic Right Ventricle Dysplasia.Circulation  2003; 108:2302.
  20. Nasir K, tufail K, Bomma C, Tandri H, Roguin A, Tichnell C, James C, Kasper E, Tomaselli G, Spevak P, Calkins H. Value of a Prolonged S Wave Upstroke in ECG Leads V1-V3 in Differentiating Patients with ARVD From those with Idiopathic Ventricular Tachycardia.  J Am Coll Cardiol 2003;
  21. Piccini J, Nassir K, Bomma C, Dalal D, Tandri H, Tichnell C, James C, Calkins H. Electrocardiographic Evidence of Progression of Arrhythmogenic Right Ventricular Dysplasia.  Heart Rhythm 2004;1:S20(63).
  22. Dalal D, Bomma C, Daya S, Prakasa K, Nasir K, Tandri H, James C, Tichnell C, Crosson J, Calkins H. Clinical Profile of Arrhythmogenic Right Ventricular Dysplasia Cardiomyopathy:  A Report of 50 Cases from the United States.  Heart Rhythm  2004;1:S162(514).
  23. Bomma C, Fritz J, Dalal D, Tandri H, Nasir K, Calkins H, Bluemke D.  Normal Morphological Variants of Right Ventricle on Magnetic Resonance Imaging.  Heart Rhythm 2004;1:S132(416).
  24. Prakasa K, Tandri H, Dalal D, Bomma C, Rosen B, Edvardsen T, Corretti M, Calkins H, Abraham T. Diagnostic Value of Tissue Doppler Imaging in Arrhythmogenic Right Ventricular Dysplasia.  Heart Rhythm 2004;1:S21(66).
  25. Prakasa K, Dalal D, Bomma C, Corretti M, Calins H.  Exercise Induced ST-Segment Elevation in Arrhythmogenic Right Ventricular Dysplasia.  Hearth Rhythm 2004;1:S20(62).
  26. Tandri H, Saranathan M, Rodriquez R, Bomma C, Nasir K, Rosen B, Calkins H, Lima J, Blumeke D. Non-invasive Detection of Myocardial Fibrosis in Arrhythmogenic Right Ventricular Cardiomyopathy Using Delayed Enhancement MR Imaging:  Correlation with Histopathology.  Heart Rhythm 2004;1:S21(65).
  27. Bomma C, Tandri H, Edvardsen T, Rosen B, Dalal D, Nasir K, Prakasa K, Lima J, Calkins H. Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy-A Bi-Ventricular Disease?  Heart Rhythm 2004;1:S164(520).
  28. Bomma C, Piccini J, Dalal D, Ahmed D, Tandri H, Nasir K, Tichnell C, James C, Rutberg J, Calkins H.  Electrocardiographic Progression of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy (ARVD/C).  J Am Coll Cardiol  2004;43:109A.
  29. Bomma C, Rosen B, Tandri H, Lima J, Stuber M. Transmural Difference of Diastolic Function in Physiological Hypertrophy versus Pathological Hypertrophy using Tagged Magnetic Resonance Imaging.  J Am Coll Cardiol  2004; 43:370A.
  30. Dalal D, Bomma C, Nasir K, Tandri H, James C, Tichnell C, Ahmed D, Calkins, H. Evaluation of Electrocardiography, Signal Averaged Electrocardiography, Exercise Tolerance Testing, Echocardiography and Magnetic Resonance Imaging in Diagnosis of ARVD.  J Am Coll Cardiol  2004;43:209A(1127-104).
  31.  Nasir K,  Dalal D, Bomma C, Tandri H, Ahmed D, Roguin A, Tichnell C, James C, Calkins H.  Value of SAECG and Electrophysiological Testing in Identifying ARVD Patients Who Do Receive ICD Therapy.  J Am Coll Cardiol 2004;43:142A.
  32. Nasir K, Bomma C, Tandri H, Roguin A, Dalal D, Ahmed D, Tichnell C, James C, Kasper E, Spevak P, Calkins H.  Value of Electrocardiographic Parameters in Identifying Patients with a Mild form of ARVD.  J Am Coll Cardiol 2004;43:108A.
  33. Samanthapudi D, Tandri H, Calkins H.  Long-term Outcome of Patients with Cardiac Sarcoidosis Receiving Implantable Cardioverter Defibrillators.  J Am Coll Cardiol 2004;43:126A.
  34. Samanthapudi D, Tandri H, Nasir K, Bomma C, Calkins H.  Role of Body Surface Mapping in Evaluation of Patients with Arrhythmogenic Right Ventricular Dysplasia and Right Bundle Branch Block.  J Am Coll Cardiol  2004;43:143A.
  35. Prakasa K, Dong J, Dalal D, Bomma C, Stachura R, James C, Tichnell C, Calkins H.  Body Surface Mapping – A Useful Additional Diagnostic Tool in Arrhythmogenic Right Ventricular Dysplasia.  Circulation 2004;110 (17):2158.
  36. Dalal D, Bomma C, Prakasa K, Tandri H, Piccini J, Tichnell C, James C, Calkins H.  Arrhythmogenic Right Ventricular Dysplasia:  A United States Experience.  Circulation 2004;110(17)2351.
  37. Yoerger D, Marcus F, Sherrill D, Calkins H, Zareba W, Towbin J, Moss A, The Multidisciplinary Study of ARVD Investigators, Picard M.  Quantitation of Echocardiographic Abnormalities in Individuals Meeting Task Force Criteria for Arrhythmogenic Right Ventricular Dysplasia.  Circulation 2004;110(17)2418.
  38. Prakasa K, Fernandez V, Bomma C, Dalal D, Tandri H, James C, Tichnell C, Corretti M, Calkins H, Abraham T.  Gender Differences in Tissue Doppler Velocity.  Circulation 2005;111(4)E68
  39. Prakasa K, Wang J, Tichnell C, Dalal D, Bomma C, Tandri H, James C, Calkins H, Abraham T.  Role of Tissue Doppler Imaging in the Early Diagnosis of Arrhythmogenic Right Ventricular Dysplasia.  Circulation 2005;112(17)
  40. Bomma C, Calkins H, Cannom D, Dalal D, Daubert J, Duff H, Estes M, Krahn A, Marcus F, Scheinman M, Talajic M, Wilber D, Zareba W, Bluemke D; Multidisciplinary Study of Right Ventricular Dysplasia Investigators.  Cardiac MRI findings in patient with Arrhythmogenic Right Ventricular Dysplasia:  A report from the Multidisciplinary Study of Right Ventricular Dysplasia.  Circulation 2005;112(17)2;1521.
  41. Piccini J, Dalal D, Roguin A, Bomma C, Cheng A, Prakasa K, Tichnell C, James C, Russell S, Crosson J, Bluemke D, Calkins H.  Primary and Secondary Prevention of Sudden Cardiac Death in Arrhythmogenic Right Ventricular Dysplasia.  Circulation 2005;112(17)
  42. Dalal D, Molin LH, Piccini J, Bomma C, Prakasa K, Tichnell C, James C, Calkins H,  Judge DP. Clinical Features of ARVD Associated with Mutations in PKP2.  Circulation 2005; 112(17)
  43. Dalal D, Prakasa K, Bomma C, Dong J, Nasir K, Tichnell C, James C, Calkins H.  Sudden Cardiac Death in Patients with Arrhythmogenic Right Ventricular Dysplasia:  A Series of 31 Cases from United States.  J Am Coll Cardiol 2005;45:1106(3A)
  44. Prakasa K, Bomma C, Dalal D, Tandri H, Wang J, Tichnell C, James C,  Corretti M, Bluemki D, Calkins H, Abraham T.  Three-dimensional Echocardiography in Arrhythmogenic Right Ventricular Dysplasia.  J Am Coll Cardiol 2005;45:1053(3A)
  45. Macedo R, Prakasa K, Tandri H, Marcus F, Calkins H, Lima J, Bluemke D.  MRI Findings in Patients with Fat Dissociation Syndrome of the Right Ventricle who did not meet the Task Force Criteria for Arrhythmogenic Right Ventricular Dysplasia.  J Cardiovasc Magnetic Res 2006;8:117-210.
  46. Macedo R, Prakasa K, Tandri H, Marcus F, Calkins H, Lima J, Bluemke D.  Evaluation of Tricuspid Annulus Systolic Plane Excursion with MRI in Arrhythmogenic Right Ventricular Dysplasia Patients.   J Cardiovasc Magnetic Res 2006;8:211-300.
  47. Prakasa K, Wang J, Dalal D, James C, Tichnell C, Calkins H, Abraham T.  Tissue Doppler is Superior to Conventional Echocardiography in the Diagnosis of Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy.  J Am Coll Cardiol 2006, 47:(4)A.
  48. Prakasa K, Wang J, Tandri H, Dalal D, James C, Tichnell C, Tucker A, Calkins H, Abraham T.  Tissue Doppler and Strain Echocardiography – A Sensitive Imaging Technique to Diagnose Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy.  Accepted for Featured poster session, Heart Rhythm, 2006
  49. Prakasa K, Wange J, Tichnell C, James C, Dalal D, Bluemke D, Corretti M, Judge D, Calkins H, Abraham T.  Tissue Doppler and Strain Echocardiography in Arrhythmogenic Right Ventricular Dysplasia.  J Am Soc Echo 2006
  50. Dalal D, James C, Devanagondi R, Tichnell C, Tucker A, Prakasa K, Calkins H, Judge DP.  Penetrance of Mutations in Plakophilin-2 among Families with Arrhythmogenic Right Ventricular Dysplasia.  Accepted, HRS May, 2006
  51. Prakasa K, Dalal D, Judge D, Calkins H, Abraham T.  Strain Echocardiography Suggests Plakophilin-2 Mutation is Associated with a Milder Functional Phenotype in Arrhythmogenic Right Ventricular Dysplasia.  Presented, AHA 2006
  52. Wang J, Prakasa K, Tandri H, Bomma C, James C, Tichnell C, Bluemke D, Calkins H, Abraham T.  Tissue Velocity and Fractional Area Change Independently Predict Right Ventricular Ejection Fraction Determined by Cardiac Magnetic Resonance.  Moderated Poster, ASE 2006
  53. Corrado D, Leoni L, Calkins H, Favale S, Ward D, Boriani G, Link MS, Ricci S, Piccini JP, Basso C, Dalal D, Estes NA, Santini M, Buja G, McKenna WJ, Thiene G, Iliceto S.  Prophylactic Implantable Defibrillator in Patients with Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia and No Prior Sustained Ventricular Tachyarrhythmias:  Therapy-Based Risk Stratification During a Long Term Follow-up.  Circulation 2006
  54. Prakasa K, Tandri H, Dimaano VL, Dalal D, Tichnell C, James C, Calkins H, Abraham T.  Tissue Doppler and Strain Imaging Suggests Right Ventricular Mechanical Dyssynchrony in Arrhythmogenic Right Ventricular Dysplasia.  Poster, Heart Rhythm 2007
  55. Prakasa K, Dalal D, Tandri H, Tichnell C, James C, Calkins H, Abraham T.  Left Ventricular Regional Functional Assessment in Arrhythmogenic Right Ventricular Dysplasia Using Automated Functional Imaging.  Poster, Heart Rhythm 2007
  56. Jain R, Shaker E, Dong J, Sinha S, Calkins H, Darshan D.  Incremental yield of repeat radiofrequency catheter ablation procedures for the management of ventricular tachycardia in arrhythmogenic right ventricular dysplasia/ cardiomyopathy. Journal of Cardiovascular Electrophysiology Volume18,Supplement 2 October 2007.(Presented at Venice Arrhythmia 2007).
  57. Macedo R, Tandri H, Tichnell C, Zareba W, Marcus F, Calkins H, Bluemke DA.  The Multidisciplinary Study of Right Ventricular Dysplasia: MRI findings in Family Members of Affected Individuals. Journal of Cardiovascular Magnetic Resonance 2007, Volume 9 Issue 2: 175-326.
  58. Dalal D, Tandri H, James C, Tichnell C, Abraham T, Russell S, Judge D, Bluemke D, Calkins H. Comprehensive Cardiac Magnetic Resonance Imaging in Family Members of Desmosomal Mutation-Associated Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy Patients Reveals a Possible Early Sign of the Disease. Circulation 2007;116:II_391.
    1. Tandri H, Dalal D, Jain A, Judge D, Abraham T, James C, Daya S, Tichnell C, Russell S, Calkins H, Bluemke D. Magnetic Resonance Imaging Reveals Novel Phenotypic Expression of Desmosomal Mutation in First-Degree Relatives of Patients with Arrhythmogenic Right Ventricular Dysplasia (ARVD). Prevalence and Clinical Significance in Patients Evaluated for ARVD. Circulation. 2007;116:II_374. – Young Investigator Award.